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Primary Hepatic Leiomyosarcoma with Giant Cyst Formation : A Case Report

フォーマット:
論文
責任表示:
Rokutanda, Nana ; Makita, Fujio ; Ohwada, Susumu ; Sakamoto, Ichiro ; Yoshimura, Sumihiko ; Togo, Nozomi ; Takeyoshi, Izumi ; Morishita, Yasuo
言語:
英語
出版情報:
北関東医学会, 2005-05-01
著者名:
Rokutanda, Nana
Makita, Fujio
Ohwada, Susumu
Sakamoto, Ichiro
Yoshimura, Sumihiko
Togo, Nozomi
Takeyoshi, Izumi
Morishita, Yasuo
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掲載情報:
The Kitakanto medical journal = 北関東医学
ISSN:
1343-2826  CiNii Research  Webcat Plus  JAIRO
巻:
55
通号:
2
開始ページ:
165
終了ページ:
168
バージョン:
VoR
概要:
application/pdf<br />Journal Article<br />A 64-year-old male with right upper abdominal pain had been treated with an H2-blocker for three months as a gastric ulcer recurrence with no response. An abdominal US identified a large cystic tumor in the left lobe of the liver. Tumor markers were all normal ; hepatitis serology tests were all negative, although liver function tests were elevated slightly. A CT scan showed a well-defined cystic tumor with a thick, heterogeneously enhanced wall. Selective celiac artery angiograms showed displacement of the common hepatic artery, and an avascular area. As a malignant tumor was suspected, a left lobectomy of the liver was performed. The tumor measured 17×15×12cm and contained central cystic degeneration filled with 280 ml of dark red fluid. Microscopic findings revealed anaplastic spindle cell proliferation, and immunohistochemical examination was positive for α-smooth muscle actin. A thorough survey did not detect a primary tumor in any other organ. Therefore, primary hepatic leiomyosarcoma was diagnosed. Only 80 cases have been reported. We reviewed the available literature. 続きを見る
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